%0 Journal Article %T Congenital afibrinogenemia: a case report of a spontaneous hepatic hematoma %+ Université Sorbonne Paris Cité (USPC) %+ Anesthésie réanimation et Médecine d'urgence %+ Service de dermatologie [CHU d'Amiens-Picardie] %+ Mécanismes physiopathologiques et conséquences des calcifications vasculaires - UR UPJV 7517 (MP3CV) %+ CHU Amiens-Picardie %A Malaquin, Stephanie %A Rebibo, Lionel %A Chivot, Cyril %A Badoux, Louise %A Mahjoub, Yazine %A Dupont, Herve %< avec comité de lecture %@ 0025-7974 %J Medicine %I Lippincott, Williams & Wilkins %V 95 %N 28 %8 2016 %D 2016 %R 10.1097/MD.0000000000004150 %Z Life Sciences [q-bio]Journal articles %X Introduction: Afibrinogenemia is a rare coagulation disorder. Clinical features of spontaneous bleeding, bleeding after minor trauma, or after surgery have been described as well as thrombo-embolic complications. In this article, we presented the case of a 19-year old female with congenital afibrinogenemia who was admitted with a spontaneous intrahepatic hematoma. Conclusions: Supportive treatment including transfusion and fibrinogen administration, associated with repeated packing surgeries and selective embolization, were successfully performed. %G English %L hal-03575529 %U https://u-picardie.hal.science/hal-03575529 %~ UNIV-PICARDIE %~ U-PICARDIE %~ MP3CV